CLINICAL GUIDELINES for CONGENITAL HEART DISEASE Contributors ADULT CHD CARE RESOURCES Editors: Mary Rummell, MN, RN, CNS, CPNC Editor 2011, 2014 and 2016 Clinical Nurse Specialist, Cardiac Services Oregon Health and Science University Sandy Staveski, PhD, RN, CPNP-AC/PC, CNS, CCRN Editor 2011 Nurse Scientist, Research in Patient Services, Heart Institute Contributors: Diana Arias, MSN, ARNP, FNP-C, CPN Clinical Specialist, Miami Children s Hospital Kathryn Barrett, NP-C, RN, CCRN Nurse Practitioner, Pediatric Loren Brown, BSN, RN, CCRN Clinical Nursing Educator, Cardiovascular Catheterization Lab Louise Callow RN, MSN, CPNP Nurse Practitioner, Pediatric Cardiac Surgery University of Michigan, CS Mott Children s Center CS Mott Children s Hospital Ann Arbor, Michigan Andrea Frederick, RN, NP Nurse Practitioner, Adult Congenital Cardiology Stanford Hospital and Clinics Palo Alto, California NEONATAL AND PEDIATRIC CARE RESOURCES Editors: Mary Rummell, MN, RN, CNS, CPNP, FAHA Editor 2014 and 2016 Clinical Nurse Specialist, Cardiac Services Oregon Health and Science University Dorothy M Beke, MS, RN, CPNP-PC/AC Editor 2014 and 2016 Clinical Nurse Specialist, Mechanical Circulatory Support Resource, Boston Melissa B Jones, MSN, RN, APRN, CPNP-AC Editor 2016 Sandy Staveski, PhD, RN, CPNP-AC/PC, CNS, CCRN Editor 2014 Nurse Scientist, Research in Patient Services, Heart Institute Project Leads: Mary Rummell, MN, RN, CNS, CPNP, FAHA Project Lead 2014 and 2016 Clinical Nurse Specialist, Cardiac Services Oregon Health and Science University Dorothy M Beke, RN, MS, CPNP-PC/AC Project Lead 2014 and 2016 Clinical Nurse Specialist, Mechanical Circulatory Support Resource, 1
Annette Haynes, MS, RN, CNS, CCRN Cardiology Clinical Nurse Specialist, Stanford Hospital and Clinics Palo Alto, California Lindsey Katzmark, MSN, RN, APNP Nurse Practitioner, Adult Congenital Heart Disease Program Children s Hospital of Wisconsin Milwaukee, Wisconsin Mary Rummell, MN, RN, CNS, CPNP, FAHA Clinical Nurse Specialist, Cardiac Services Oregon Health and Science University Jo Ann Nieves, MSN, CPN, ARNP, PNP-BC Nurse Practitioner, Adult Congenital Heart Program Miami Children s Hospital Nancy Rudd, MS, RN, CPNP-AC/PC Nurse Practitioner, Pediatric Cardiology Adult Congenital Heart Disease Program Children s Hospital of Wisconsin Milwaukee, Wisconsin Margaret Schroder, RN, PNP-BC Nurse Practitioner, Cardiovascular Surgery Services, Heart Institute Sandy Staveski, PhD, RN, CPNP-AC/PC, CNS, CCRN Nurse Scientist, Research in Patient Services, Heart Institute Melissa B Jones, MSN, RN, APRN, CPNP-AC Project Lead 2016 Christine Riley, MSN, APRN, CPNP-AC Project Lead 2016 Louise Callow, MSN, RN, CPNP Project Lead 2014 and 2016 Nurse Practitioner, Pediatric Cardiac Surgery University of Michigan Congenital Heart Hospital Ann Arbor, Michigan Cecilia St. George-Hyslop, M Ed, BScN, RN, CNCCP (C) Project Lead 2014 and 2016 Advanced Nursing Practice Educator The Labatt Family Heart Centre The Hospital for Sick Children Toronto, Ontario, Canada Bronwyn Bartle, DNP, CPNP-AC/PC Project Lead 2016 Pediatric Nurse Practitioner, Duke Children s Pediatric and Congenital Heart Center Durham, North Carolina Dawn Tucker MSN, RN, CPNP-AC Project Lead 2014 Director, Heart Center Advanced Practice Nurse, Children s Mercy Hospital and Clinics Kansas City, Missouri Contributors: Luisa F. Angel, ARNP, PPCNP-BC Nurse Practitioner, Nicklaus Children s Hospital Heart Program Annierose D. Abogadie BSN, RN, CCRN, RN-BC Clinical Manger, 2
Catherine Baxter, MSN, RN, CPNP-AC Pediatric Nurse Practitioner, Pediatric Cardiac Surgery Levine Children s Hospital Charlotte, North Carolina Dorothy M Beke, RN, MS, CPNP-PC/AC Clinical Nurse Specialist, Mechanical Circulatory Support Resource, Angela Blankenship, RN, MS, CPNP-PC/AC Nationwide Children s Hospital Columbus, Ohio Lindsey Bradbury, BSN, RN, CCRN Nursing Department Director, Pediatric Intensive Care Unit Children s Mercy Hospitals and Clinics Kansas City, Missouri Erin Burke, MSN, RN, PNP Nurse Practitioner, Cardiology Preoperative Clinic Boston, MA Patricia Burke, BSN, CCRN Staff Nurse III, Boston, MA Louise Callow, MSN, RN, CPNP Nurse Practitioner, Pediatric Cardiac Surgery University of Michigan, CS Mott Children s Hospital Ann Arbor, Michigan Christine Chiu-Man, MSc, RCT, RCES, CEPS, CCDS, FHRS Team Lead, EP Pacemaker Technologist Hospital for Sick Children Toronto, Canada Jason Corcoran, PharmD, BCPS Manager, Clinical Pharmacy Services, Clinical Specialist, 3
Meghan Cusick, MSN, RN, NP-C Nurse Practitioner, Cardiology Preoperative Clinic Boston, MA Elizabeth S Daley, BSN, RN, BA, CCRN Staff Nurse III, Cardiothoracic Intensive Care Unit Children s Hospital of Los Angeles T. Lynn Dees, MNSc, APRN, PNP-BC, CPNP-AC Advanced Practice Nurse, Pediatric Cardiology University of Arkansas for Medical Sciences Arkansas Children s Hospital Little Rock, Arkansas Amy Donnellan, MSN, CPNP-AC Clinical Nurse Specialist, Misty Ellis, MSN, APRN Pediatric Nurse Practitioner, University of Louisville and Kosair Children s Hospital Department of Pediatric Critical Care Louisville, Kentucky Andrea Frederick, NP Nurse Practitioner, Adult Congenital Cardiology, Stanford Hospital and Clinics Stanford, California (original author) Amanda Green, MSN, ARNP, FNP-C Nurse Practitioner, Cardiac Catheterization Laboratory Nicklaus Children s Hospital Melanie Guerrero, MSN, RN, CPN Patient Care Services Clinical Manager, Cardiovascular Acute Unit Los Angelis, California Nancy Hagberg, MS, RN, FNP Nurse Practitioner, Child Heart Associates 4
Worcester, Massachusetts Ashley Harlow, BSN, RN, CCRN Clinical Educator, Jenna Heichel, MSN, APRN, CPNP-AC Flerida Imperial-Perez, MN, RN, CNS-BC, CCNS-P Patient Care Services Clinical Manager, Clinical Nurse Specialist Cardiothoracic Intensive Care Unit Los Angelis, California Melissa B Jones, MSN, RN, APRN, CPNP-AC Lindsey Justice, MSN, RN, CPNP-AC Kim Kellogg, MS, RN, CPNP Pediatric Nurse Practitioner, Pediatric Cardiac Surgery University of Michigan Congenital Heart Center CS Mott Children s Hospital Ann Arbor, Michigan Jeannie Koo, RN, CPNP-AC Nurse Practitioner, Pediatric Critical Care Duke Children s Hospital Durham, North Carolina Linda M. Lambert, MSN, RN, CFNP Nurse Practitioner, Pediatric Cardiothoracic Surgery Primary Children s Hospital Salt Lake City, Utah Patricia Lincoln, MS, RN, CCRN, CNS-BC Clinical Nurse Specialist, 5
Grace Macek, MSN, RN, PNP-BC Pediatric Nurse Practitioner, Cardiac and Thoracic Surgery University of Chicago Medicine, Comer Children s Hospital Chicago, Illinois Megan Matiasek, MS, RN, CPNP-PC/AC Sandra McGill-Lane, MSN,RN, FNP, CCRN Clinical Nurse Specialist, Pediatric Morgan Stanley s Children s Hospital of New York Presbyterian New York, New York Amber Merritt, MSN, RN, RN-BC, CCRN Clinical Coordinator, Justine Mize, MSN, RN, CCRN, CPN Professional Practice Specialist, Debra Forbes Morrow, BSN, RN, CCRN Staff Nurse Level III, Infection Prevention Coordinator, Children s Hospital Boston Candace Morton, MSN, RN, APNP Pediatric Nurse Practitioner, Electrophysiology Children s Hospital of Wisconsin Milwaukee, Wisconsin Catherine Murphy, BSN, RN Staff Nurse, Cardiac Critical Care Unit Labatt Family Heart Center Hospital for Sick Children Toronto, Canada 6
Jenna Murray, MSN, RN, CPNP-AC Ventricular Assist Device Coordinator/ Heart Failure Nurse Practitioner Lucile Packard Children s Hospital Stanford Palo Alto, California Casey Naughton, MS, RN, BSN, CPNP-AC Nurse Practitioner, Children s Heart Program University of Maryland Medical Center Baltimore, Maryland Jennifer Newcombe, MSN, CNS, CPNP-PC/AC Nurse Practitioner, Pediatric Cardiothoracic Surgery Loma Linda University Hospital Loma Linda, California Jo Ann Nieves, MSN, CPN, ARNP, PNP-BC, FAHA Nurse Practitioner, Cardiology Nicklaus Children s Hospital Melissa Olen, MSN, ARPN, FNP-C, CCRN Electrophysiology Nurse Practitioner, Coordinator of Remote Device Clinic Nicklaus Children s Hospital Nida Oriza, RN, BSN Core Charge Nurse, Emily Peterson, RN, NP Lurie Children s Hospital Chicago, Illinois Courtney Petro, RN, BSN, CCRN Staff Nurse, Pediatric Lucile Packard Children s Hospital at Stanford Palo Alto, California Nida Sulit-Oriza, BSN, RN Clinical Nurse IV, Core Charge Nurse Cardiothoracic Intensive Care Unit 7
Christine M. Rachwal, MSN, RN, CCRN Clinical Nurse Specialist, Christine Riley, MSN, APRN, CPNP-AC Kaye Remo, RN Staff Nurse, University of California San Francisco Benioff Children s Hospital San Francisco, California Gwen Rempel, PhD, RN Associate Professor, Faculty of Health Disciplines Athabasca University Associate Adjunct Professor, Faculty of Nursing, University of Alberta Associate Adjunct Professor, Department of Pediatrics, University of Alberta Alberta, Canada Christine Riley, MSN, APRN, CPNP-AC Mary Rummell, MN, RN, CPNP, CNS, FAHA Clinical Nurse Specialist, Pediatric Cardiology, Cardiac Services Oregon Health & Science University (Retired) Melanie Sojka, MSN, RN, CPNP-AC/PC Advanced Practice Nurse/Pediatric Nurse Practitioner, Pediatric Cardiac Surgery University of Chicago Medicine, Comer Children s Hospital Chicago, Illinois Jennifer Strawn, BSN, RN, CPN Nurse Clinician, Pediatric Cardiology Children s Hospital & Medical Center Omaha, Nebraska Cecelia St. George-Hyslop, M Ed, RN, BA Gen, CNCCPC 8
Advanced Practice Nurse Educator, Cardiac Critical Care Unit Labatt Family Heart Center Hospital for Sick Children Toronto, Canada Svetlana Streltsova MSN, RN, CCRN Clinical Nurse III, Pediatric Morgan Stanley Children s Hospital of New York Presbyterian New York, New York Kristen Sullivan, MSN, RN, CPNP-AC Nurse Practitioner, Cardiothoracic Surgery Phoenix Children s Hospital Heart Center Phoenix, Arizona Alisa Tortorich, RD, CSP, CNSC, LD Board Certified Specialist in Pediatric Nutrition Certified Nutrition Support Clinician Doernbecher Children s Hospital Victoria Winter, RN, MSN, CNS, CCRN Clinical Nurse IV, Cardiothoracic Intensive Care Unit Adjunct Professor Azusa Pacific University School of Nursing Azusa, California 9